Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome(Herlyn-Werner-Wunderlich Syndrome): A Case Report

Abstract

Herlyn-Werner-Wunderlich Syndrome (HWW), also known as Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) syndrome, is a rare Müllerian duct anomaly characterized by a triad of didelphic uterus, obstructed hemivagina, and ipsilateral renal agenesis. We report a case of a 15-year-old girl presenting with acute pelvic pain, cyclic dysmenorrhea, and a palpable abdominal mass. Imaging revealed a bicornuate uterus with a blind hemivagina, hematocolpos, and hematometra. Surgical management included resection of the vaginal septum and reconstruction, resulting in prompt recovery without complications.