A Case Report of Left Ventricular Endomyocardial Fibrosis

Authors

  • Linda Ataya Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine Author
  • Ramze Abu Arram Istishari Arab Hospital, Radiologic Technologist, Ramallah, Palestine Author
  • S Smerat Department of Medical Imaging, Faculty of Allied Medical Health, Palestine Ahliya University, Bethlehem, Palestine Author
  • Majed Dwaik Dean Medical College and Health Science, Palestine Polytechnic University, Hebron, Palestine Author
  • Nizar Awwad Cardiac Surgery Consultant Istishari Arab Hospital, Ramallah, Palestine Author
  • Nizar Awwad Cardiac Surgery Consultant Istishari Arab Hospital, Ramallah, Palestine Author
  • Shireen Zahran Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine Author
  • Raya Radi Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine Author
  • Abeer Omar Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine Author
  • Jamal Khatib Cardiac care Department at the Istishari Arab Hospital, Ramallah, Palestine Author

DOI:

https://doi.org/10.47363/JMHC/2024(6)287

Keywords:

Restrictive Cardiomyopathy, Endomyocardial Fibrosis, Heart Failure, Cardiac Surgery, Hypereosinophilia, Cardiac Magnetic Resonance

Abstract

Endomyocardial fibrosis (EMF). is a prevalent restrictive cardiomyopathy worldwide, often linked to chronic eosinophilia and dietary, environmental, and infectious factors. Its hallmark is the fibrotic obliteration of the affected ventricle, leading to restrictive physiology. The disease affects 50% of cases, often affecting the apices of the right and left ventricles and causing atrioventricular valve dysfunction. Endomyocardial fibrosis is characterized by fibrotic enlargement and thickening of the endocardium and myocardium of one or both ventricles. Massive fibrosis building of the ventricular endocardium causing architectural distortion, impaired and poor filling, and valvular insufficiency that defines the disease. Early diagnosing and treatment including surgical management and care in a suitable intensive cardiac support settings will enhance the survival rate especially in patients with advanced heart failure. Advancements in diagnostic imaging techniques and availability of new pharmacological choices and interfering with surgical managements as soon as possible whenever needed, defining the targeted and potential populations will support disease prevention and early diagnosis, all will contribute to lower the rates of morbidity and mortality.

Author Biographies

  • Linda Ataya, Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine

    Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine 

  • Ramze Abu Arram, Istishari Arab Hospital, Radiologic Technologist, Ramallah, Palestine

    Istishari Arab Hospital, Radiologic Technologist, Ramallah, Palestine

  • S Smerat, Department of Medical Imaging, Faculty of Allied Medical Health, Palestine Ahliya University, Bethlehem, Palestine

    Department of Medical Imaging, Faculty of Allied Medical Health, Palestine Ahliya University, Bethlehem, Palestine

  • Majed Dwaik, Dean Medical College and Health Science, Palestine Polytechnic University, Hebron, Palestine

    Dean Medical College and Health Science, Palestine Polytechnic University, Hebron, Palestine

  • Nizar Awwad, Cardiac Surgery Consultant Istishari Arab Hospital, Ramallah, Palestine

    Cardiac Surgery Consultant Istishari Arab Hospital, Ramallah, Palestine 

  • Nizar Awwad, Cardiac Surgery Consultant Istishari Arab Hospital, Ramallah, Palestine

    Cardiac Surgery Consultant Istishari Arab Hospital, Ramallah, Palestine

  • Shireen Zahran, Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine

    Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine

  • Raya Radi, Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine

    Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine 

  • Abeer Omar, Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine

    Pediatrics Department at the Istishari Arab Hospital, Ramallah, Palestine 

  • Jamal Khatib, Cardiac care Department at the Istishari Arab Hospital, Ramallah, Palestine

    Cardiac care Department at the Istishari Arab Hospital, Ramallah, Palestine

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Published

2024-11-11