Delayed Contrast Enhancement On Cardiac MRI In a CASE of Steinert Disease: A Case Report

Abstract

Type 1 myotonic dystrophy (Steinert’s disease) is a genetic syndrome characterized by progressive muscular weakness and multisystemic repercussions. Cardiac conduction abnormalities are frequently seen, but the incidence of dilated cardiomyopathy and heart failure seems to be less common. Current evidence suggests that subclinical cardiomyopathy can be demonstrated by means of cardiac magnetic resonance imaging (CMRI). We 
present a 31-year-old man with genetically established muscular dystrophy 1 and no signs of cardiac involvement. CMRI revealed intramyocardial and pericardial contrast uptake in some regions. The meaning of these findings should be investigated in order to understand and prevent future complications