Primary Epithelioid Angiosarcoma of the Thyroid: Long-Term Survival Case Report and Literature Review

Authors

  • Reverberi Chiara Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine, Italy. Author
  • Parisi Giuseppe Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy. Author
  • De Pellegrin Alessandro Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine, Italy. Author
  • Ceschia Tino Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy. Author
  • Pizzolitto Stefano Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy. Author
  • Trovò Marco Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy. Author

DOI:

https://doi.org/10.47363/JCRR/2021(3)132

Keywords:

Epithelioid, Thyroid, Long-Term Survival

Abstract

Thyroid angiosarcoma is a rare neoplasm of debated clinical management. In addition, the epithelioid variant poses microscopic challenges due to its close resemblance to poorly differentiated carcinoma. Only 63 cases of thyroid angiosarcoma have been published in English literature. Due to its rarity, the limited clinical experience can make its management complex. We report a new case of primary thyroid angiosarcoma showing preponderant epithelioid
features characterized by an exceptional long survival. We also provide a discussion on the role of radiotherapy in tumor treatment and a brief review of the pertinent literature. 

Author Biographies

  • Reverberi Chiara, Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine, Italy.


    Reverberi Chiara, Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine, Italy.

  • Parisi Giuseppe, Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.


    Parisi Giuseppe, Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.

  • De Pellegrin Alessandro, Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine, Italy.

    De Pellegrin Alessandro, Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine, Italy.

  • Ceschia Tino, Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.

    Ceschia Tino,Institute of Radiation Oncology-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.

  • Pizzolitto Stefano, Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.


    Pizzolitto Stefano, Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.

  • Trovò Marco, Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.


     Trovò Marco, Institute of Pathologic Anatomy-Azienda Sanitaria Universitaria Friuli Centrale, Ospedale Santa Maria della Misericordia, Udine,Italy.

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Published

2021-03-03