A Multiple Sclerosis Mimiker with Good Recovery following Specific Therapy: Susac Syndrome

Abstract

Susac Syndrome (SuS) is a rare disease, characterized by an autoimmune endothelopathy, that involves brain, retina and inner ear. We describe a case of a young woman affected by inner ear-predominant SuS, initially suspected for demyelinating disease, with delayed diagnosis and irreversible hearing ischemic damage, but good prognosis, treated according to current recommendations