The Congenital Absence of the Portal Vein

Authors

  • M Lagrine Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco Author
  • A Bourrahouat Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco Author
  • I Ait Sab Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco Author
  • M Sbihi Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco Author

DOI:

https://doi.org/10.47363/JPRRR/2020(2)116

Keywords:

Absence of Portal Vein, Gastrointestinal Tract Hemorrhage, Esophageal Varices

Abstract

Congenital absence of the portal vein (CAPV) is a rare defect often accompanied by other abnormalities such as heart defect, skeletal anomalies and / or
liver tumors [1]. 

We describe here a case of CAPV revealed by an upper gastrointestinal tract hemorrhage in a child aged 02 years and 8 months. The esogatro-duodenal fibroscopy revealed the presence of Esophageal varices grade II, abdominal ultrasound revealed a large liver with no visualization of the spleen. Subsequent abdominal computed tomography revealed the presence of a spleno-mesaraic trunk measuring 7 mm in anteroposterior diameter receiving the inferior and superior mesenteric vein and a small splenic vein draining by dilated peri-gastric and peri-esophageal leads. Associated with splenic hypoplasia and portal trunk atresia. The rest of the malformative assessment was negative.

Author Biographies

  • M Lagrine, Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

    Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

  • A Bourrahouat, Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

    Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

  • I Ait Sab, Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

    Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

  • M Sbihi, Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

    Pediatric B Department, Mohammed VI university Hospital, Marrakesh, Morocco

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Published

2020-12-30

Issue

Vol. 2 No. 4 (2020): Volume 2 Issue 4

Section

Articles