Familial Complete Atrioventricular Block (FCAVB) DDDR PacemakerImplant with Synchromax

Authors

  • Carlos Rodríguez Artuza Department of Cardiology. Hospital Coromoto Maracaibo, Venezuela. Sagrada Familia Clinical Center Maracaibo, Venezuela Author
  • Mayela Labarca Department of Cardiology. Hospital Coromoto Maracaibo, Venezuela. Sagrada Familia Clinical Center Maracaibo, Venezuela Author

DOI:

https://doi.org/10.47363/JVMS/2023(1)101

Keywords:

Atrioventricular Block, Pacemaker, Inheritance

Abstract

We present the case of a family with complete atrioventricular block involving several generations, with autosomal dominant Mendelian inheritance, where one of those long-term affected presents heart failure. This entity corresponds to progressive familial heart block type I, mainly described in South Africa. Permanent Pacemaker implant using Synchromax was successful.

Author Biographies

  • Carlos Rodríguez Artuza, Department of Cardiology. Hospital Coromoto Maracaibo, Venezuela. Sagrada Familia Clinical Center Maracaibo, Venezuela

    Department of Cardiology. Hospital Coromoto Maracaibo, Venezuela. Sagrada Familia Clinical Center Maracaibo, Venezuela

  • Mayela Labarca, Department of Cardiology. Hospital Coromoto Maracaibo, Venezuela. Sagrada Familia Clinical Center Maracaibo, Venezuela

    Department of Cardiology. Hospital Coromoto Maracaibo, Venezuela. Sagrada Familia Clinical Center Maracaibo, Venezuela

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Published

2023-03-15